Pheochromocytoma/Chromaffin Tumor/Chromaffinoma/Chromaffinparaganglionoma

Pheochromocytoma/Chromaffin Tumor/Chromaffinoma/Chromaffinparaganglionoma

Last Reviewed : 12/24/2020
Pheochromocytoma/Chromaffin Tumor/Chromaffinoma/Chromaffinparaganglionoma

Pheochromocytoma is a neuroendocrine tumor of the adrenal glands that can release high levels of epinephrine and norepinephrine. The signs and symptoms are palpitations, increased heart rate, increased BP, weight loss, diaphoresis etc. It can also cause resistant arterial hypertension, be fatal if it causes a hypertensive emergency. Up to 25% of pheochromocytomas may be familial. Mutations of the genes VHL, RET, NF1, SDHB and SDHD are all known to cause familial pheochromocytoma. It is a tumor of the multiple endocrine neoplasia syndrome, type IIA and type IIB. The incidence is 2 to 8 per million persons per year, present in 0.1% to 1% of patients with hypertension and it is present in approximately 5% of patients with incidentally discovered adrenal masses. The peak incidence occurs in the third to fifth decades of life and is equal between males and females.

We researched this topic for you and found the following best online resources. They are categorized into basic, advanced, and research level based on the extent of information you need. You will be taken to the respective websites by pressing on the links below.


Basic information: medscape, pheochromocytoma patient, phaeochromocytoma mayo clinic, pheochromocytoma, pheochromocytoma onco link, all aboutpheochromocytoma medline plus, pheochromocytoma merck manuals, pheochromocytoma health line, pheochromocytoma webmd, pheochromocytoma american association of endocrine surgeons, pheochromocytoma (adrenaline-producing adrenal tumor), neuroendocrine tumor– overview

Advanced information: biomed central, pheochromocytomas and secreting paragangliomas ajr, pheochromocytoma: the range of appearances on ultrasound, ct, mri, and functional imaging, american journal of roentgenology. 2013;200: 370-378. 10.2214/ajr.12.9126 nih, hypertension in pheochromocytoma: characteristics and treatment nih, national cancer institute, pheochromocytoma and paraganglioma treatment pheochromocytoma: recommendations for clinical practice from the first international symposium, doi:10.1038/ncpendmet0396 recent advances in genetics, diagnosis, localization, and treatment of pheochromocytoma, ann intern med. 2001;134(4):315-329. doi:10.7326/0003-4819-134-4-200102200-00016


Research: nejm, germ-line mutations in nonsyndromicpheochromocytoma, doi: 10.1056/nejmoa020152 journal of the national cancer institute, pheochromocytoma: the expanding genetic differential diagnosis, jnci j natl cancer inst (2003) 95(16): 1196-1204.doi: 10.1093/jnci/djg024 pheochromocytoma is characterized by catecholamine-mediated myocarditis, focal and diffuse myocardial fibrosis, and myocardial dysfunction, j am collcardiol. 2016;67(20):2364-2374. doi:10.1016/j.jacc.2016.03.543 international journals of surgery case reports, pheochromocytoma as a rare cause of arterial hypertension in a patient with autosomal dominant polycystic kidney disease: a diagnostic and therapeutic dilemma, doi: pheochromocytoma treated by laparoscopic surgery, thoracic involvement withpheochromocytoma, chest. 1999;115(2):511-521. doi:10.1378/chest.115.2.511 pheochromocytoma: current approaches and future directions, the oncologist, doi:10.1634/theoncologist.2008-0043 plos, targeting heat shock protein 90 for the treatment of malignant pheochromocytoma, jcem, megacolon as the presenting feature in pheochromocytoma european urology, pheochromocytoma in urologic practice radiographics, pheochromocytoma: an imaging chameleon, doi:;year=2015;volume=31;issue=3;spage=317;epage=323;aulast=ramakrishna. pheochromocytoma resection: current concepts in anesthetic management, journal of anaesthesiology clinical pharmacology, doi: 10.4103/0970-9185.161665 the journal of clinical investigations, tyrosine hydroxylase in human adrenal and pheochromocytoma: localization, kinetics, and catecholamine inhibition


Related topics: nord, pheochromocytoma adrenal tumors endocrine web

Other articles: omim the doctors

Other helpful resources: pheochromocytoma support board neuroendocrine tumor research foundation pheochromocytoma and paraganglioma research support organization pheochromocytoma support foundation pheopara troopers

Related videos: youtube, pheochromocytoma youtube,pheochromocytoma, pheochromocytomas: an extremely dangerous tumor youtube, histopathology adrenal—pheochromocytoma youtube, pheochromocytoma youtube, diagnosis of pheochromocytomas youtube, laparoscopic left adrenalectomy for pheochromocytoma youtube, robotic adrenal sparing pheochromocytoma removal youtube, integrated genomic characterization of pheochromocytoma and paraganglioma - matthew wilkerson


Presentation/quiz/newspaper articles: slideshare, powerpoint on pheochromocytoma slideshare, pheochromocytoma prezi, pheochromocytoma prezi, pheochromocytoma physiology prezi, pheochromocytoma

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